Utrophin-dystrophin-deficient mice as a model for Duchenne muscular dystrophy

  • A E Deconinck
  • , J A Rafael
  • , J A Skinner
  • , S C Brown
  • , A C Potter
  • , L Metzinger
  • , D J Watt
  • , J G Dickson
  • , J M Tinsley
  • , K E Davies

Research output: Contribution to journalArticlepeer-review

Original languageEnglish
Pages (from-to)717-727
Number of pages11
JournalCell
Volume90
Issue number4
Publication statusPublished - 1997

Keywords

  • Animals
  • Cytoskeletal Proteins
  • Disease Models, Animal
  • Dystrophin
  • Female
  • Male
  • Membrane Proteins
  • Mice
  • Mice, Inbred mdx
  • Muscle, Skeletal
  • Muscular Dystrophy, Animal
  • Myosin Heavy Chains
  • Neuromuscular Junction
  • Receptors, Cholinergic
  • Tendons
  • Utrophin

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